Web Feature Service (WFS) is a protocol for accessing geospatial data stores such as databases and Shapefiles over the Web. However, WFS does not provide direct access to data distributed in multiple servers. In addition, WFS features extracted from...
While OGC’s WFS facilitates disseminating heterogeneous spatial data over the Web and allows feature-level geospatial information sharing and synchronization, performance issues challenge the efficient and effective utilization of WFS for disaster re...
The foundry industry in South Africa forms one of the greatest industries in the manufacturing sector. It produces waste foundry sand (WFS) that ends up in landfill sites. Around 80% of the WFS could be utilized as a substitute for sand in concrete....
Background: Wolfram syndrome (WFS, OMIM: #222300) is an ultrarare autosomal recessive disorder characterized by diabetes insipidus, diabetes mellitus, optic nerve atrophy and deafness. It has been reported that the average retinal thickness in WFS pa...
Wolfram Syndrome (WFS) is a rare, autosomal, recessive neurogenetic disorder that affects many organ systems. It is characterised by diabetes insipidus, diabetes mellites, optic atrophy, and deafness and, therefore, is also known as DIDMOAD. Nearly 1...
In order to improve the properties of wood flour (WF)/poly(lactic acid) (PLA) 3D-printed composites, WF was treated with a silane coupling agent (KH550) and acetic anhydride (Ac2O), respectively. The effects of WF modification and the addition of acr...
The WFS1 gene was first identified in Wolfram Syndrome 1 (WS1), a rare autosomal recessive genetic disorder characterized by severe and progressive neurodegenerative changes. WFS1’s role in various cellular mechanisms, particularly in calcium h...
Background: WFS1-spectrum disorders are caused by a mutation in the WFS1 gene. The term includes a wide range of rare disorders, from the most severe Wolfram syndrome with autosomal recessive inheritance to milder clinical manifestations with a...
Coronavirus disease COVID-19, which is caused by severe acute respiratory syndrome coronavirus SARS-CoV-2, has become a worldwide pandemic in recent years. In addition to being a respiratory disease, COVID-19 is a ‘vascular disease’ since...
Tungsten fiber-reinforced Zr41.25Ti13.75Cu12.5Ni10Be22.5 amorphous matrix composites (hereinafter referred to as Wf/Zr-based amorphous matrix composites) are considered as a potential new generation of projectile material, while the penetration behav...
Background/Objectives: A heterozygous mutation in the WFS1 gene is responsible for autosomal dominant non-syndromic hearing loss (DFNA6/14/38) and Wolfram-like syndrome, which is characterized by bilateral sensorineural hearing loss with optic atroph...
The aim of this study is to contribute to a better description of the genotypic and phenotypic spectrum of DFNA6/14/38 and aid in counseling future patients identified with this variant. Therefore, we describe the genotype and phenotype in a large Du...
Large scale production of water-intensive industrial products can intensify water scarcity, resulting in potential unsustainable water use at local and regional scales. This study proposes a methodological framework for assessing the WF sustainabilit...
Wolfram syndrome (WS) 1 is a rare monogenic neurodegenerative disorder caused by mutations in the gene encoding WFS1. Knowledge of the pathophysiology of WS is incomplete and to date, there is no treatment available. Here, we describe early deviation...
Timely monitoring and mapping of salt-affected areas are essential for the prevention of land degradation and sustainable soil management in arid and semi-arid regions. The main objective of this study was to develop Synthetic Aperture Radar (SAR) po...
This work is a collaborative effort between academia and industry to promote the development of new sustainable and profitable materials for manufacturing products. Incorporating wood flour particles (WF) in polypropylene (PP) grants environmental ad...
Wind farm (WF) equivalence is an effective method to achieve accurate and efficient simulation of large-scale WF. Existing equivalent models are generally suitable for one certain or very few scenarios, and have difficulty reflecting the multiple asp...
The primary objective of this research is to utilize an industrial waste byproduct such as waste foundry sand (WFS) as an alternative for fine aggregate in self-compacting concrete (SCC). This research focuses on the use of WFS in SCC to enhance dura...
A tungsten fiber/Zr-based bulk metallic glass matrix composite (Wf/Zr-MG) is a potential penetrator material. To compare and analyze the penetration behavior of Wf/Zr-MG and a tungsten heavy alloy (WHA), a penetration experiment into the 30CrMnMo hom...
Natural rubber (NR) is extensively utilized in numerous industries, such as aerospace, military, and transportation, because of its exceptional elasticity and all-around mechanical qualities. However, commercial NR made using various techniques typic...
Affected by climate warming and anthropogenic disturbances, the thermo-mechanical stability of warm and ice-rich frozen ground along the Qinghai–Tibet Railway (QTR) is continuously decreasing, and melting subsidence damage to existing warm froz...
The error threshold is the cornerstone to balance the mathematical complexity and simulation speed of wind farm (WF) equivalent models, and can promote the standardization process of equivalent methodology. Due to differences in power system conditio...
The blue water footprint (WF) is an indicator of freshwater required to produce a given end product. Determining the blue WF for milk production, the seasonal water use and the impact of water conservation are important sustainability considerations...
In order to further explore the feasibility of the application of the residue of Chinese herbal medicine in FDM 3D technology and enrich the kinds of printing materials, Astragalus residue powder(ARP)/poly(lactic acid) (PLA) biocomposite was FDM 3D-p...
The utilization of wind energy sources with energy storage systems has been increased in the power sector to satisfy the consumer’s energy demand with minimum price. This paper presents the impact of a wind farm (WF) and pumped hydroelectric storage...
In order to adapt to the launch velocity of modern artillery, it is necessary to study the fracture mechanism of the high-velocity penetration of penetrators. Therefore, the penetration fracture mode of tungsten-fiber-reinforced Zr-based bulk metalli...
Factors promoting thrombosis such as von Willebrand factor (vWF) and P-selectin are essential for the development of atherosclerosis (AS) and arterial thrombosis. The processing, maturation and release of vWF are regulated by autophagy of vascular en...
Background and Objectives: Elevated von Willebrand factor (vWF) levels have been reported in malaria, but their relationship with disease severity remains unclear. This study aimed to compare vWF levels between Plasmodium-infected and uninfected indi...
In recent years, the rapid development of tourism in China’s arid areas has led to a continuous increase in water consumption, heightening the tension between water supply and demand in the region. For this reason, drought-type tourist destinat...
N6-methyladenosine (m6A) is the most common modification in eukaryotic RNAs. Growing research indicates that m6A methylation is crucial for a multitude of biological processes. However, research on the m6A modifications in the regulation of porcine m...
7 May 2021
The Water–Food Nexus (WF) has been proposed to reach equitable, balanced, and sustainable access to water and food resources in the face of the growing population demand. Therefore, developing models to assess them has become more relevant. This work...
In this paper, an optimal transient control (OTC) scheme is proposed to improve the transient stability of the grid-forming (GFM) wind farm (WF) based on the transient stability of the WTs. The converter’s current operating safety range is cons...
Endowing wind farms (WFs) with fault ride through (FRT) capability is crucial to their continuous availability under various operating conditions. This paper proposes a dynamic adaptive multi-cell fault current limiter (MCFCL) topology to enhance the...
The objective of this study is to use wheat flour (WF) and hydroxymethyl melamine prepolymer (HMP) to develop a low cost, highly water-resistant, starch-based bio-adhesive for plywood fabrication. Three-layer plywood was fabricated using the resultan...
According to the grid code specifications, low voltage ride-through (LVRT) is one of the key factors for grid-tied wind farms (WFs). Since fixed-speed wind turbines with squirrel cage induction generators (FSWT-SCIGs) require an adequate quantity of...
Planning logistical processes supports the managerial processes of an enterprise, including investments such as wind farm construction. The aim of the article is to analyze and assess the time determinant in the logistical process of wind farm planni...
Polar format algorithm (PFA) is a widely used high-resolution SAR imaging algorithm that can be implemented in advanced widefield staring synthetic aperture radar (WFS-SAR). However, existing algorithms have limited analysis in wavefront curvature er...
Human platelets play a vital role in haemostasis, pathological bleeding and thrombosis. The haemostatic mechanism is concerned with the control of bleeding from injured blood vessels, whereby platelets interact with the damaged inner vessel wall to f...
Biallelic mutations in the gene encoding WFS1 underlie the development of Wolfram syndrome (WS), a rare neurodegenerative disorder with no available cure. We have previously shown that Wfs1 deficiency can impair the functioning of the renin-angiotens...
This study investigates the long-term mechanical and microstructural behavior of high-performance concrete (HPC), incorporating hybrid mixtures of coal bottom ash (CBA) and waste foundry sand (WFS) as sustainable mineral additives. The experimental p...
The bottom ash of a municipal solid waste incinerator (MSWI) and water filter silt (WFS) were applied to a controlled low-strength material (CLSM) in the present study. The CLSM of the control group was composed of cement, water, and fine aggregates....
21 February 2022
Wolfram syndrome 1, a rare autosomal recessive neurodegenerative disease, is caused by mutations in the WFS1 gene. It is characterized by diabetes insipidus, diabetes mellitus, optic atrophy, and deafness (DIDMOAD), and other clinical manifestations...
The current study aims to examine the impact of non-work responsibilities (NWRs) due to work from home (WfH) conditions on the work–life imbalance (WLI) and emotional exhaustion (EE) experienced by pregnant working women during the pandemic (CO...
A multiscale sample entropy (MSE) algorithm is presented as a time domain feature extraction method to study the vocal behavior of blue whales through continuous acoustic monitoring. Additionally, MSE is applied to the Gaussian mixture model (GMM) fo...
In wavefront sensorless adaptive optics (WFS-less AO) systems, stochastic parallel gradient descent (SPGD) is the primary optimization method for correcting wavefront distortions. However, as the intensity of atmospheric turbulence interference incre...
Background: Early neurovascular unit (NVU) impairment plays a critical role in the pathogenesis of diabetic retinopathy (DR), often preceding clinically detectable changes. Butyrate, a short-chain fatty acid (SCFA) derived from gut microbiota, has sh...
Background: Wolfram syndrome (WS) is an ultrarare neuroendocrine disorder caused by pathogenic variants in WFS1, frequently leading to progressive neurological, autonomic, and cognitive impairment. Anticipating neurological trajectories remains chall...
Hereditary optic neuropathy (HON) is a group of genetically heterogeneous diseases that cause optic nerve atrophy and lead to substantial visual impairment. HON may present with optic nerve atrophy only or in association with various systemic abnorma...
9 March 2022
Wolfram syndrome 1 (WS1) is a rare neurodegenerative disease transmitted in an autosomal recessive mode. It is characterized by diabetes insipidus (DI), diabetes mellitus (DM), optic atrophy (OA), and sensorineural hearing loss (D) (DIDMOAD). The cli...
Life cycle assessments (LCAs) play a strategic role in improving the environmental performance of a company and in supporting a successful marketing communication. The high impact of the food industry on natural resources, in terms of water consumpti...
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