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Case Report

Isolated Intracranial Hypertensions as Onset of Myelin Oligodendrocyte Glycoprotein Antibody Disease

1
Developmental Neurology Unit, Bambino Gesù Children’s Hospital IRCCS, 00165 Rome, Italy
2
Functional and Interventional Neuroradiology Unit, Bambino Gesù Children’s Hospital IRCCS, 00165 Rome, Italy
3
Neuroradiology Unit, NESMOS Department Sant’Andrea Hospital, La Sapienza University, Via di Grottarossa, 1035-1039, 00189 Rome, Italy
4
Department of Diagnostics and Laboratory Medicine, Medical Laboratory Unit, Unit of Allergy and Autoimmunity, Bambino Gesù Children’s Hospital, IRCCS, 00165 Rome, Italy
5
Department of Pediatrics, University of Perugia, 06123 Perugia, Italy
6
Systems Medicine Department, Hospital of Rome, Tor Vergata University, 00133 Rome, Italy
7
Center for Sensory Motor Interaction, Aalborg University, DK-9220 Aalborg, Denmark
*
Author to whom correspondence should be addressed.
J. Clin. Med. 2024, 13(15), 4468; https://doi.org/10.3390/jcm13154468
Submission received: 20 June 2024 / Revised: 25 July 2024 / Accepted: 29 July 2024 / Published: 30 July 2024
(This article belongs to the Special Issue Advances in Child Neurology)

Abstract

Myelin oligodendrocyte glycoprotein antibody disease (MOGAD) is characterized by multiple phenotypic conditions such as acute disseminated encephalomyelitis, optic neuritis, and myelitis. MOGAD’s spectrum is expanding, with potential symptoms of increased intracranial pressure that are similar to idiopathic intracranial hypertension (IIH). We report a boy with new-onset continuous headache and a brain MRI at onset suggesting idiopathic intracranial hypertension (IIH). The patient showed resistance to treatment with acetazolamide and, after one month, developed optic neuritis in the left eye. Laboratory tests documented positive MOG antibodies (anti-MOG) in the serum. The final diagnosis was MOGAD, with the initial symptoms resembling IIH.
Keywords: idiopathic intracranial hypertension; pseudotumor cerebri; secondary headache; MOGAD; MOG antibodies idiopathic intracranial hypertension; pseudotumor cerebri; secondary headache; MOGAD; MOG antibodies

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MDPI and ACS Style

Papetti, L.; Moltoni, G.; Longo, D.; Monte, G.; Dellepiane, F.; Pro, S.; Bracaglia, G.; Ruscitto, C.; Verrotti, A.; Valeriani, M. Isolated Intracranial Hypertensions as Onset of Myelin Oligodendrocyte Glycoprotein Antibody Disease. J. Clin. Med. 2024, 13, 4468. https://doi.org/10.3390/jcm13154468

AMA Style

Papetti L, Moltoni G, Longo D, Monte G, Dellepiane F, Pro S, Bracaglia G, Ruscitto C, Verrotti A, Valeriani M. Isolated Intracranial Hypertensions as Onset of Myelin Oligodendrocyte Glycoprotein Antibody Disease. Journal of Clinical Medicine. 2024; 13(15):4468. https://doi.org/10.3390/jcm13154468

Chicago/Turabian Style

Papetti, Laura, Giulia Moltoni, Daniela Longo, Gabriele Monte, Francesco Dellepiane, Stefano Pro, Giorgia Bracaglia, Claudia Ruscitto, Alberto Verrotti, and Massimiliano Valeriani. 2024. "Isolated Intracranial Hypertensions as Onset of Myelin Oligodendrocyte Glycoprotein Antibody Disease" Journal of Clinical Medicine 13, no. 15: 4468. https://doi.org/10.3390/jcm13154468

APA Style

Papetti, L., Moltoni, G., Longo, D., Monte, G., Dellepiane, F., Pro, S., Bracaglia, G., Ruscitto, C., Verrotti, A., & Valeriani, M. (2024). Isolated Intracranial Hypertensions as Onset of Myelin Oligodendrocyte Glycoprotein Antibody Disease. Journal of Clinical Medicine, 13(15), 4468. https://doi.org/10.3390/jcm13154468

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