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  • Case Report
  • Open Access

30 October 2017

6 Pages

Sarcoidosis-Associated Pulmonary Hypertension Treated with Sildenafil

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1
1st Department of Lung Diseases, National Tuberculosis and Lung Diseases Research Institute, Warsaw, Poland
2
Department of Radiology, National Tuberculosis and Lung Diseases Research Institute, Warsaw, Poland
3
Department of Respiratory Physiopathology, National Tuberculosis and Lung Diseases Research Institute, Warsaw, Poland
4
Department of Cardiovascular and Pulmonary Thromboembolic Diseases CMKP, European Health Centre Otwock, Otwock, Poland

Abstract

Development of sarcoidosis-associated pulmonary hypertension (SAPH) significantly worsens prognosis in sarcoidosis patients. Unfortunately, there is no treatment of proven benefit for this condition. Medications used for treatment of pulmonary arterial hypertension are of great interest in this respect. Here, we report a case of a patient with severe SAPH treated with sildenafil. A significant, but only temporary improvement in functional status was observed, and the patient died of gradually progressing heart and respiratory failure while awaiting for lung transplantation.

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