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Case Report

Dental Prosthetic Rehabilitation of Papillon-Lefèvre Syndrome: A Case Report

by
Shweta M. Patil
1,
Suryakant B. Metkari
2,
Shilpa Shetty
3,
Savita Thakkannavar
2,
Sachin C. Sarode
4,*,
Gargi S. Sarode
4,
Namrata Sengupta
4 and
Shankargouda Patil
5
1
Department of Prosthodontics, Tatyasaheb Kore Dental College and Research Center, Kolhapur, Maharashtra, India
2
Department of Oral Pathology and Microbiology, Tatyasaheb Kore Dental College and Research Center, Kolhapur, Maharashtra, India
3
Department of Conservative Dentistry, Tatyasaheb Kore Dental College and Research Center, Kolhapur, Maharashtra, India
4
Department of Oral Pathology and Microbiology, Dr. D.Y. Patil Dental College and Hospital, Dr. D.Y. Patil Vidyapeeth, Pimpri, Pune, India
5
Department of Maxillofacial Surgery and Diagnostic Sciences, Division of Oral Pathology, College of Dentistry, Jazan University, Jazan, Saudi Arabia
*
Author to whom correspondence should be addressed.
Clin. Pract. 2020, 10(3), 1285; https://doi.org/10.4081/cp.2020.1285
Submission received: 23 July 2020 / Revised: 24 August 2020 / Accepted: 7 September 2020 / Published: 21 September 2020

Abstract

Papillon-Lefèvre syndrome (PLS) is a rare disorder characterized by palmar plantar hyperkeratosis and rapidly progressive periodontitis with loss of deciduous and permanent dentition at an early age. It is reported to occur in 1 to 4 individuals per million people. This case report presents highlighting features of the rare PLS in a 17-year old male who complained of discomfort while mastication and it was accompanied with symmetrical, sharply demarcated erythematous plaques involving the skin of the palms and soles, which extended to the finger joints, elbows, and knees. Along with the rough and dry skin, hyperhidrosis of lesion with a foul odor and transverse grooving of nails were noted. The past dental history revealed normal eruption of deciduous teeth followed by pre-mature mobility and shedding in 4-6 months. Permanent teeth also showed normal eruption and early shedding in the next 4-5 years. Complete edentulous maxillary and mandibular arches led to a decrease in alveolar bone and facial heights. There was no similar disorder in the patient’s family but family history revealed the consanguineous marriage of the patient’s parents.
Keywords: palmar planter hyperkeratosis; Papillon-Lefèvre syndrome; periodontitis; complete denture palmar planter hyperkeratosis; Papillon-Lefèvre syndrome; periodontitis; complete denture

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MDPI and ACS Style

Patil, S.M.; Metkari, S.B.; Shetty, S.; Thakkannavar, S.; Sarode, S.C.; Sarode, G.S.; Sengupta, N.; Patil, S. Dental Prosthetic Rehabilitation of Papillon-Lefèvre Syndrome: A Case Report. Clin. Pract. 2020, 10, 1285. https://doi.org/10.4081/cp.2020.1285

AMA Style

Patil SM, Metkari SB, Shetty S, Thakkannavar S, Sarode SC, Sarode GS, Sengupta N, Patil S. Dental Prosthetic Rehabilitation of Papillon-Lefèvre Syndrome: A Case Report. Clinics and Practice. 2020; 10(3):1285. https://doi.org/10.4081/cp.2020.1285

Chicago/Turabian Style

Patil, Shweta M., Suryakant B. Metkari, Shilpa Shetty, Savita Thakkannavar, Sachin C. Sarode, Gargi S. Sarode, Namrata Sengupta, and Shankargouda Patil. 2020. "Dental Prosthetic Rehabilitation of Papillon-Lefèvre Syndrome: A Case Report" Clinics and Practice 10, no. 3: 1285. https://doi.org/10.4081/cp.2020.1285

APA Style

Patil, S. M., Metkari, S. B., Shetty, S., Thakkannavar, S., Sarode, S. C., Sarode, G. S., Sengupta, N., & Patil, S. (2020). Dental Prosthetic Rehabilitation of Papillon-Lefèvre Syndrome: A Case Report. Clinics and Practice, 10(3), 1285. https://doi.org/10.4081/cp.2020.1285

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