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Cardiogenetics
Volume 9
Issue 1
10.4081/cardiogenetics.2019.8194
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Cardiogenetics is published by MDPI from Volume 10 Issue 2 (2020). Previous articles were published by another publisher in Open Access under a CC-BY (or CC-BY-NC-ND) licence, and they are hosted by MDPI on mdpi.com as a courtesy and upon agreement with PAGEPress.
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Case Report

Non-Ischemic Scar Underlines Ventricular Arrhythmias in Kearns-Sayre Syndrome

by
Stefano Figliozzi
,
Alessandro Zorzi
*,
Martina Perazzolo Marra
,
Alessandro Ruocco
,
Sabino Iliceto
,
Domenico Corrado
and
Chiara Calore
Department of Cardiac, Thoracic, Vascular and Public Health Sciences, University of Padova, Italy
*
Author to whom correspondence should be addressed.
Cardiogenetics 2019, 9(1), 8194; https://doi.org/10.4081/cardiogenetics.2019.8194
Submission received: 28 March 2019 / Revised: 28 March 2019 / Accepted: 12 July 2019 / Published: 29 July 2019

Abstract

Kearns-Sayre syndrome (KSS) is a rare mitochondrial disease in which cardiac involvement has been associated with poor prognosis. Although the most common clinical manifestation is progressive conduction system impairment, patients can suffer from ventricular arrhythmias. Yet, they show a high prevalence of sudden cardiac death, whose etiopathological mechanism is not completely understood. Cardiac magnetic resonance is a rising tool to detect subclinical heart involvement in many heart diseases and was recently able to detect nonischemic scar, which is an arrhythmogenic substrate, in patients affected by KSS.
Keywords: mitochondrial cardiomyopathy; Kearns-Sayre syndrome; ventricular arrhythmias; imaging; cardiac magnetic resonance; non-ischemic scar mitochondrial cardiomyopathy; Kearns-Sayre syndrome; ventricular arrhythmias; imaging; cardiac magnetic resonance; non-ischemic scar

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MDPI and ACS Style

Figliozzi, S.; Zorzi, A.; Perazzolo Marra, M.; Ruocco, A.; Iliceto, S.; Corrado, D.; Calore, C. Non-Ischemic Scar Underlines Ventricular Arrhythmias in Kearns-Sayre Syndrome. Cardiogenetics 2019, 9, 8194. https://doi.org/10.4081/cardiogenetics.2019.8194

AMA Style

Figliozzi S, Zorzi A, Perazzolo Marra M, Ruocco A, Iliceto S, Corrado D, Calore C. Non-Ischemic Scar Underlines Ventricular Arrhythmias in Kearns-Sayre Syndrome. Cardiogenetics. 2019; 9(1):8194. https://doi.org/10.4081/cardiogenetics.2019.8194

Chicago/Turabian Style

Figliozzi, Stefano, Alessandro Zorzi, Martina Perazzolo Marra, Alessandro Ruocco, Sabino Iliceto, Domenico Corrado, and Chiara Calore. 2019. "Non-Ischemic Scar Underlines Ventricular Arrhythmias in Kearns-Sayre Syndrome" Cardiogenetics 9, no. 1: 8194. https://doi.org/10.4081/cardiogenetics.2019.8194

APA Style

Figliozzi, S., Zorzi, A., Perazzolo Marra, M., Ruocco, A., Iliceto, S., Corrado, D., & Calore, C. (2019). Non-Ischemic Scar Underlines Ventricular Arrhythmias in Kearns-Sayre Syndrome. Cardiogenetics, 9(1), 8194. https://doi.org/10.4081/cardiogenetics.2019.8194

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