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1 Result Found

  • Article
  • Open Access
7 Citations
4,334 Views
16 Pages

Hyperinsulinemic Hypoglycemia in Three Generations of a Family with Glucokinase Activating Mutation, c.295T>C (p.Trp99Arg)

  • Aleksandra Gilis-Januszewska,
  • Anna Bogusławska,
  • Artur Kowalik,
  • Ewelina Rzepka,
  • Karolina Soczówka,
  • Elwira Przybylik-Mazurek,
  • Bogusław Głowa and
  • Alicja Hubalewska-Dydejczyk

1 October 2021

Familial Hyperinsulinemic Hypoglycemia (FHH) is a very rare disease with heterogeneous clinical manifestations. There are only a few reports of heterozygous activating mutations of glucokinase (GCK) attributable to FHH, with no reports describing eff...