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Case Report

Acquired Cardiovascular Diseases in Patients with Pulmonary Hypertension Due to Congenital Heart Disease: A Case Report

by
Eglė Ereminienė
1,2,3,*,
Mantvydas Stuoka
1,
Rasa Ordienė
1,
Jurgita Plisienė
1,
Skaidrius Miliauskas
4 and
Eglė Tamulėnaitė
1,2
1
Department of Cardiology, Medical Academy, Lithuanian University of Health Sciences, LT-44307 Kaunas, Lithuania
2
Laboratory of Clinical Cardiology, Institute of Cardiology, Lithuanian University of Health Sciences, LT-50162 Kaunas, Lithuania
3
Society of Cardiologists of Kaunas Region, LT-50103, Kaunas, Lithuania
4
Department of Pulmonology, Medical Academy, Lithuanian University of Health Sciences, LT-44307 Kaunas, Lithuania
*
Author to whom correspondence should be addressed.
Medicina 2024, 60(2), 266; https://doi.org/10.3390/medicina60020266
Submission received: 13 December 2023 / Revised: 29 January 2024 / Accepted: 1 February 2024 / Published: 3 February 2024
(This article belongs to the Special Issue Pulmonary Hypertension: Symptoms, Diagnosis and Management)

Abstract

Background: Advances in the diagnosis and treatment of congenital heart diseases (CHDs) have resulted in improved survival rates for CHD patients. Up to 90% of individuals with mild CHD and 40% with complex CHD now reach the age of 60. Previous studies have indicated an elevated risk of atherosclerotic cardiovascular disease (ASCVD) and associated risk factors, morbidity, and mortality in adults with congenital heart disease (ACHD). However, there were no comprehensive guidelines for the prevention and management of acquired cardiovascular diseases (CVDs) in ACHD populations until recently. Case presentation: A 55-year-old man with Eisenmenger syndrome and comorbidities (arterial hypertension, heart failure, dyslipidemia, hyperuricemia, and a history of pulmonary embolism (PE)) presented with progressive breathlessness. The electrocardiogram (ECG) revealed signs of right ventricle (RV) hypertrophy and overload, while echocardiography showed reduced RV function, RV overload, and severe pulmonary hypertension (PH) signs, and preserved left ventricle (LV) function. After ruling out a new PE episode, acute coronary syndrome (ACS) was diagnosed, and percutaneous intervention was performed within 24–48 h of admission. Conclusions: This case highlights the importance of increased awareness of acquired heart diseases in patients with pulmonary hypertension due to CHD.
Keywords: adult congenital heart diseases; pulmonary hypertension; acquired heart diseases; prevention and management adult congenital heart diseases; pulmonary hypertension; acquired heart diseases; prevention and management

Share and Cite

MDPI and ACS Style

Ereminienė, E.; Stuoka, M.; Ordienė, R.; Plisienė, J.; Miliauskas, S.; Tamulėnaitė, E. Acquired Cardiovascular Diseases in Patients with Pulmonary Hypertension Due to Congenital Heart Disease: A Case Report. Medicina 2024, 60, 266. https://doi.org/10.3390/medicina60020266

AMA Style

Ereminienė E, Stuoka M, Ordienė R, Plisienė J, Miliauskas S, Tamulėnaitė E. Acquired Cardiovascular Diseases in Patients with Pulmonary Hypertension Due to Congenital Heart Disease: A Case Report. Medicina. 2024; 60(2):266. https://doi.org/10.3390/medicina60020266

Chicago/Turabian Style

Ereminienė, Eglė, Mantvydas Stuoka, Rasa Ordienė, Jurgita Plisienė, Skaidrius Miliauskas, and Eglė Tamulėnaitė. 2024. "Acquired Cardiovascular Diseases in Patients with Pulmonary Hypertension Due to Congenital Heart Disease: A Case Report" Medicina 60, no. 2: 266. https://doi.org/10.3390/medicina60020266

APA Style

Ereminienė, E., Stuoka, M., Ordienė, R., Plisienė, J., Miliauskas, S., & Tamulėnaitė, E. (2024). Acquired Cardiovascular Diseases in Patients with Pulmonary Hypertension Due to Congenital Heart Disease: A Case Report. Medicina, 60(2), 266. https://doi.org/10.3390/medicina60020266

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