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Brief Report

Segmental Pulmonary Hypertension in Children with Congenital Heart Disease

1
Department of Pediatric Cardiology, Baylor College of Medicine, Texas Children’s Hospital Austin Specialty Care, Austin, TX 78759, USA
2
Department of Pediatric Cardiology, University of Colorado Health Science Center, Children’s Hospital of Colorado, Denver, CO 80045, USA
*
Author to whom correspondence should be addressed.
Medicina 2020, 56(10), 492; https://doi.org/10.3390/medicina56100492
Submission received: 26 August 2020 / Revised: 21 September 2020 / Accepted: 22 September 2020 / Published: 24 September 2020
(This article belongs to the Special Issue Focused Update on Pulmonary Hypertension in Children)

Abstract

Segmental pulmonary hypertension is a complex condition in children that encompasses many congenital heart diseases including pulmonary atresia with ventricular septal defect, hemitruncus/truncus arteriosus with branch pulmonary artery stenosis, unilateral absent pulmonary artery, and several post-tricuspid shunt lesions. Multimodality imaging is required to confirm and assess pulmonary vascular disease in subjects with major aorto-pulmonary collaterals. We describe 3 children with complex congenital heart defects who have a variable degree of segmental pulmonary hypertension and discuss management strategies and the role of interventional and/or pulmonary hypertension targeted therapies.
Keywords: pulmonary hypertension in children; congenital heart disease; segmental pulmonary hypertension; digital subtraction angiography pulmonary hypertension in children; congenital heart disease; segmental pulmonary hypertension; digital subtraction angiography

Share and Cite

MDPI and ACS Style

Das, B.B.; Frank, B.; Ivy, D. Segmental Pulmonary Hypertension in Children with Congenital Heart Disease. Medicina 2020, 56, 492. https://doi.org/10.3390/medicina56100492

AMA Style

Das BB, Frank B, Ivy D. Segmental Pulmonary Hypertension in Children with Congenital Heart Disease. Medicina. 2020; 56(10):492. https://doi.org/10.3390/medicina56100492

Chicago/Turabian Style

Das, Bibhuti B., Benjamin Frank, and Dunbar Ivy. 2020. "Segmental Pulmonary Hypertension in Children with Congenital Heart Disease" Medicina 56, no. 10: 492. https://doi.org/10.3390/medicina56100492

APA Style

Das, B. B., Frank, B., & Ivy, D. (2020). Segmental Pulmonary Hypertension in Children with Congenital Heart Disease. Medicina, 56(10), 492. https://doi.org/10.3390/medicina56100492

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