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Characterization of Patients with Pulmonary Arterial Hypertension: Data from the Polish Registry of Pulmonary Hypertension (BNP-PL)

Department of Cardiac and Vascular Diseases, Jagiellonian University Medical College, John Paul II Hospital in Krakow, Ul. Prądnicka 80, 31-202 Krakow, Poland
Department of Pulmonary Hypertension, Thromboembolic Diseases and Cardiology, Centre of Postgraduate Medical Education, 05-400 Otwock, Poland
Department of Cardiology Provincial Specialist Hospital Research and Development Center, 51-124 Wrocław, Poland
Cardiology Department, Medical University of Lodz, 91-347 Lodz, Poland
Department of Cardiology, Poznan University of Medical Sciences, 61-701 Poznan, Poland
3rd Department of Cardiology, Faculty of Medical Sciences in Zabrze, Medical University of Silesia, 41-800 Katowice, Poland
Department of Congenital Heart Disease Institute of Cardiology, 04-628 Warsaw, Poland
Department of Internal Medicine and Cardiology, Medical University of Warsaw, 02-005 Warsaw, Poland
Department of Cardiology, Cardinal Wyszynski Hospital, 20-718 Lublin, Poland
Department of Cardiology and Electrotherapy Medical University of Gdansk, 80-211 Gdansk, Poland
2nd Department of Cardiology, Faculty of Health Sciences, Collegium Medicum, Nicolaus Copernicus University, 85-168 Bydgoszcz, Poland
I Katedra i Klinika Kardiologii, Wydział Lekarski w Katowicach, Śląski Uniwersytety Medyczny w Katowicach, 40-635 Katowice, Poland
Department of Cardiology, Medical University of Lublin, 20-090 Lublin, Poland
2nd Department of Cardiology, School of Medicine with Dentistry Division in Zabrze, Medical University of Silesia in Katowice, 41-800 Zabrze, Poland
Department of Cardiology, Medical University of Bialystok, 15-276 Bialystok, Poland
Department of Cardiology, Pomeranian Medical University, Szczecin, 70-111 Szczecin, Poland
Pulmonary Department, University of Warmia and Mazury, 10-357 Olsztyn, Poland
Department of Invasive Cardiology, Polish Academy of Sciences, Mossakowski Medical Research Centre, Central Clinical Hospital of the Ministry of Interior, 02-507 Warsaw, Poland
Department of Cardiology, School of Health Sciences, Medical University of Cardiology in Katowice, 40-635 Katowice, Poland
Oddział Kardiologii i Kardiologii Inwazyjnej, Oddział Intensywnego Nadzoru Kardiologicznego, Samodzielny Publiczny Wojewódzki Szpital Zespolony w Szczecinie, 71-455 Szczecin, Poland
Department of Cardiology and Internal Medicine, Military Institute of Medicine in Warsaw, 04-141 Warsaw, Poland
Department of Cardiology, Copper Health Center, 59-300 Lubin, Poland
Department of Population Medicine and Civilization Diseases Prevention, Medical University of Bialystok, 15-269 Bialystok, Poland
Author to whom correspondence should be addressed.
J. Clin. Med. 2020, 9(1), 173;
Received: 3 December 2019 / Revised: 21 December 2019 / Accepted: 3 January 2020 / Published: 8 January 2020
Current knowledge of pulmonary arterial hypertension (PAH) epidemiology is based mainly on data from Western populations, and therefore we aimed to characterize a large group of Caucasian PAH adults of Central-Eastern European origin. We analyzed data of incident and prevalent PAH adults enrolled in a prospective national registry involving all Polish PAH centers. The estimated prevalence and annual incidence of PAH were 30.8/mln adults and 5.2/mln adults, respectively and they were the highest in females ≥65 years old. The most frequent type of PAH was idiopathic (n = 444; 46%) followed by PAH associated with congenital heart diseases (CHD-PAH, n = 356; 36.7%), and PAH associated with connective tissue disease (CTD-PAH, n = 132; 13.6%). At enrollment, most incident cases (71.9%) were at intermediate mortality risk and the prevalent cases had most of their risk factors in the intermediate or high risk range. The use of triple combination therapy was rare (4.7%). A high prevalence of PAH among older population confirms the changing demographics of PAH found in the Western countries. In contrast, we found: a female predominance across all age groups, a high proportion of patients with CHD-PAH as compared to patients with CTD-PAH and a low use of triple combination therapy. View Full-Text
Keywords: pulmonary arterial hypertension; registry; epidemiology; prevalence; incidence pulmonary arterial hypertension; registry; epidemiology; prevalence; incidence
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Kopeć, G.; Kurzyna, M.; Mroczek, E.; Chrzanowski, Ł.; Mularek-Kubzdela, T.; Skoczylas, I.; Kuśmierczyk, B.; Pruszczyk, P.; Błaszczak, P.; Lewicka, E.; Karasek, D.; Mizia-Stec, K.; Tomaszewski, M.; Jacheć, W.; Ptaszyńska-Kopczyńska, K.; Peregud-Pogorzelska, M.; Doboszyńska, A.; Pawlak, A.; Gąsior, Z.; Zabłocka, W.; Ryczek, R.; Widejko-Pietkiewicz, K.; Waligóra, M.; Darocha, S.; Furdal, M.; Ciurzyński, M.; Kasprzak, J.D.; Grabka, M.; Kamiński, K.; Hoffman, P.; Podolec, P.; Torbicki, A. Characterization of Patients with Pulmonary Arterial Hypertension: Data from the Polish Registry of Pulmonary Hypertension (BNP-PL). J. Clin. Med. 2020, 9, 173.

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