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Volume 83
Issue 6
10.5603/PiAP.2015.0074
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Advances in Respiratory Medicine is published by MDPI from Volume 90 Issue 4 (2022). Previous articles were published by another publisher in Open Access under a CC-BY (or CC-BY-NC-ND) licence, and they are hosted by MDPI on mdpi.com as a courtesy and upon agreement with Via Medica.
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Background:
Case Report

Atypical Image of Pulmonary Alveolar Proteinosis—A Case Report

by
Justyna Fijołek
*,
Elżbieta Wiatr
,
Lucyna Opoka
,
Piotr Rudziński
,
Małgorzata Nierebińska
,
Małgorzata Szołkowska
and
Kazimierz Roszkowski-Śliż
The Third Department of Pneumonology, National Research Institute of Tuberculosis and Lung Diseases, Płocka 26, 01-138 Warsaw, Poland
*
Author to whom correspondence should be addressed.
Adv. Respir. Med. 2015, 83(6), 453-456; https://doi.org/10.5603/PiAP.2015.0074
Submission received: 2 July 2015 / Revised: 10 November 2015 / Accepted: 10 November 2015 / Published: 10 November 2015

Abstract

Pulmonary alveolar proteinosis is a very rare interstitial lung disease caused by abnormal intra-alveolar surfactant accumulation. Usually, it appears as a “crazy-paving” pattern on high-resolution computed tomography. The image is so typical, that together with the characteristic bronchoalveolar lavage examination with presence of Periodic Acid Schiff positive substance is sufficient for establishing diagnosis, without histological confirmation. We present the case of the young woman with severe dyspnoea suspected of acute hypersensitivity pneumonia. The computed tomography showed numerous intralobular nodules uniformly distributed troughout the lungs. Treatment by corticosteroids had no clinical effect and next computed tomography showed progression. Despite the high risk of complications (patient had a respiratory failure), a surgical lung biopsy was performed and the histopathological diagnosis of pulmonary alveolar proteinosis was made. The whole lung lavage procedure performed twice caused regression of radiological lesions and respiratory failure.
Keywords: respiratory failure; pulmonary alveolar proteinosis; computed tomography; whole lung lavage respiratory failure; pulmonary alveolar proteinosis; computed tomography; whole lung lavage

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MDPI and ACS Style

Fijołek, J.; Wiatr, E.; Opoka, L.; Rudziński, P.; Nierebińska, M.; Szołkowska, M.; Roszkowski-Śliż, K. Atypical Image of Pulmonary Alveolar Proteinosis—A Case Report. Adv. Respir. Med. 2015, 83, 453-456. https://doi.org/10.5603/PiAP.2015.0074

AMA Style

Fijołek J, Wiatr E, Opoka L, Rudziński P, Nierebińska M, Szołkowska M, Roszkowski-Śliż K. Atypical Image of Pulmonary Alveolar Proteinosis—A Case Report. Advances in Respiratory Medicine. 2015; 83(6):453-456. https://doi.org/10.5603/PiAP.2015.0074

Chicago/Turabian Style

Fijołek, Justyna, Elżbieta Wiatr, Lucyna Opoka, Piotr Rudziński, Małgorzata Nierebińska, Małgorzata Szołkowska, and Kazimierz Roszkowski-Śliż. 2015. "Atypical Image of Pulmonary Alveolar Proteinosis—A Case Report" Advances in Respiratory Medicine 83, no. 6: 453-456. https://doi.org/10.5603/PiAP.2015.0074

APA Style

Fijołek, J., Wiatr, E., Opoka, L., Rudziński, P., Nierebińska, M., Szołkowska, M., & Roszkowski-Śliż, K. (2015). Atypical Image of Pulmonary Alveolar Proteinosis—A Case Report. Advances in Respiratory Medicine, 83(6), 453-456. https://doi.org/10.5603/PiAP.2015.0074

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