Comprehensive Cardiovascular Management of Myotonic Dystrophy Type 1 Patients: A Report from the Italian Neuro-Cardiology Network
Abstract
:1. Introduction
Myotonic Dystrophy
2. Cardiovascular Involvement in MD1
2.1. Conduction System Disease
2.2. Atrial Fibrillation (AF)
2.3. Ventricular Arrhythmias
2.4. Sudden Cardiac Death
2.5. Cardiomyopathy and Heart Failure
2.6. Hypotension
2.7. Stroke and Systemic Embolism
3. Non-Invasive Cardiac Evaluation
3.1. Twelve Lead ECG
3.2. 24 h Holter ECG Monitoring
3.3. Transthoracic Echocardiogram
3.4. Cardiac Magnetic Resonance
4. Invasive Cardiac Evaluation and Treatment
4.1. Electrophysiological Study
4.2. Loop Recorder
4.3. Pacemaker
4.4. Implantable Cardioverter-Defibrillator (ICD)
4.5. CIED Remote Monitoring
5. Open Issues/Improvement Areas in the Organization of Services
6. Disease Management Model: The “Neuro-Cardiac Team”
7. Quality Improvement and Risk Management
8. Integrated Interdisciplinary Comprehensive MD1 Pathway
9. Perspective
Author Contributions
Funding
Institutional Review Board Statement
Informed Consent Statement
Conflicts of Interest
References
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Quality Set Measures Proposed for MD1 Patients from the Italian Neuro-Cardiology Network (INCN) |
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MD1 Planning and Patient Engagement |
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Russo, V.; Antonini, G.; Massa, R.; Casali, C.; Mauriello, A.; Martino, A.M.; Marconi, R.; Garibaldi, M.; Franciosa, P.; Zecchin, M.; et al. Comprehensive Cardiovascular Management of Myotonic Dystrophy Type 1 Patients: A Report from the Italian Neuro-Cardiology Network. J. Cardiovasc. Dev. Dis. 2024, 11, 63. https://doi.org/10.3390/jcdd11020063
Russo V, Antonini G, Massa R, Casali C, Mauriello A, Martino AM, Marconi R, Garibaldi M, Franciosa P, Zecchin M, et al. Comprehensive Cardiovascular Management of Myotonic Dystrophy Type 1 Patients: A Report from the Italian Neuro-Cardiology Network. Journal of Cardiovascular Development and Disease. 2024; 11(2):63. https://doi.org/10.3390/jcdd11020063
Chicago/Turabian StyleRusso, Vincenzo, Giovanni Antonini, Roberto Massa, Carlo Casali, Alfredo Mauriello, Anna Maria Martino, Roberto Marconi, Matteo Garibaldi, Pasquale Franciosa, Massimo Zecchin, and et al. 2024. "Comprehensive Cardiovascular Management of Myotonic Dystrophy Type 1 Patients: A Report from the Italian Neuro-Cardiology Network" Journal of Cardiovascular Development and Disease 11, no. 2: 63. https://doi.org/10.3390/jcdd11020063