Nutritional Management for Pediatric Biliary Atresia Patients Preparing for Liver Transplantation
Abstract
:1. Introduction
2. Functions of the Liver
2.1. Energy Metabolism
2.2. Protein Synthesis
2.3. Ammonia Detoxification
2.4. Blood Regulation, Filtration, and Processing
2.5. Fat Metabolism
2.6. Vitamin Storage and Metabolism
2.7. Fat-Soluble Vitamins
2.8. Malnutrition of Biliary Atresia Patients
2.9. Role of Medium Chain Triglycerides (MCT) Oil in Nutrition
2.10. Challenges with Fat-Soluble Vitamins
2.11. Improving the Digestibility of Fat and Fat-Soluble Vitamins via Ursodeoxycholic Acid
2.12. Weaning Foods and Solid Foods
2.13. Use of Nasogastric (NG) and Gastrostomy (G) Tubes in Biliary Atresia Patients
2.14. Enterohepatic Axis Dysfunction and the Role of Prebiotics and Probiotics
3. Conclusions
Funding
Acknowledgments
Conflicts of Interest
Abbreviations
EFAs | Essential Fatty Acids |
G | Gastrostomy |
MCT | Medium Chain Triglycerides |
NG | Nasogastric |
UDCA | Ursodeoxycholic Acid |
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Vitamin | Functions | Food Sources |
---|---|---|
Vitamin A | Eye protection, epithelial cell maintenance, cell division, growth promotion | Carrots, sweet potatoes, pumpkins, butternut squash, spinach, kale, mangoes, apricots, cantaloupes, papayas, seaweed, eggs, butter |
Vitamin D | Regulates calcium and phosphorus balance, essential for bone formation | Mushrooms, yeast, milk, eggs, butter, salmon, tuna, fortified products |
Vitamin E | Antioxidant properties, prevent oxidation of unsaturated fatty acids and vitamin A, aid iron absorption | Wheat germ, vegetable oils, margarine, shortening, almonds, sunflower seeds, hazelnuts, peanuts, broccoli, spinach, asparagus, kale, avocados, kiwis |
Vitamin K | Blood clotting | Green leafy vegetables, seaweed, eggs, meat, cheese |
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Choe, U. Nutritional Management for Pediatric Biliary Atresia Patients Preparing for Liver Transplantation. Children 2025, 12, 391. https://doi.org/10.3390/children12030391
Choe U. Nutritional Management for Pediatric Biliary Atresia Patients Preparing for Liver Transplantation. Children. 2025; 12(3):391. https://doi.org/10.3390/children12030391
Chicago/Turabian StyleChoe, Uyory. 2025. "Nutritional Management for Pediatric Biliary Atresia Patients Preparing for Liver Transplantation" Children 12, no. 3: 391. https://doi.org/10.3390/children12030391
APA StyleChoe, U. (2025). Nutritional Management for Pediatric Biliary Atresia Patients Preparing for Liver Transplantation. Children, 12(3), 391. https://doi.org/10.3390/children12030391