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Clinics and Practice
Volume 5
Issue 3
10.4081/cp.2015.768
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Clinics and Practice is published by MDPI from Volume 11 Issue 1 (2021). Previous articles were published by another publisher in Open Access under a CC-BY (or CC-BY-NC-ND) licence, and they are hosted by MDPI on mdpi.com as a courtesy and upon agreement with PAGEPress.
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Case Report

Budd-Chiari Syndrome: An Unusual Presentation of Multisystemic Sarcoidosis

by
Rym Ennaifer
1,2,*,
Dhouha Bacha
2,3,
Hayfa Romdhane
1,2,
Myriam Cheikh
1,2,
Houda Ben Nejma
1,2 and
Najet BelHadj
1,2
1
Department of Hepato-Gastro-Enterology, Mongi Slim Hospital, Tunis; Faculty of Medicine, University of Tunis El Manar, Tunis
2
Faculty of Medicine, University of Tunis El Manar, Tunis; Department of Pathology, Mongi Slim Hospital, Tunis
*
Author to whom correspondence should be addressed.
Clin. Pract. 2015, 5(3), 768; https://doi.org/10.4081/cp.2015.768
Submission received: 28 February 2015 / Revised: 28 April 2015 / Accepted: 23 June 2015 / Published: 21 December 2015

Abstract

Sarcoidosis is a multisystem granulomatous disease of unknown origin. All organs may be affected. Liver involvement is common but it is rarely symptomatic. Only a few cases of Budd- Chiari syndrome (BCS) secondary to a hepatic sarcoidosis have been described so far. We describe a case of multisystemic sarcoidosis presenting with BCS. A 42-year old female was referred to our department for chronic and anicteric cholestasis. Laboratory and imaging investigations disclosed features of chronic BCS associated with multisystemic sarcoidosis. The positive diagnosis was based on microscopic features, which showed hepatic, gastric and cutaneous non-caseating granulomas. Screening for an underlying thrombophilic disorder was negative. The diagnosis of BCS complicating hepatic sarcoidosis was the most likely. She was put on corticosteroids and anticoagulation therapy. To our knowledge, few cases of sarcoidosis-related BCS have been reported in the literature. In addition to being an uncommon presentation of sarcoidosis, this case illustrates the importance of recognizing an unusual cause of BCS and its therapeutic difficulties.
Keywords: sarcoidosis; Budd-Chiari syndrome; liver sarcoidosis; Budd-Chiari syndrome; liver

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MDPI and ACS Style

Ennaifer, R.; Bacha, D.; Romdhane, H.; Cheikh, M.; Ben Nejma, H.; BelHadj, N. Budd-Chiari Syndrome: An Unusual Presentation of Multisystemic Sarcoidosis. Clin. Pract. 2015, 5, 768. https://doi.org/10.4081/cp.2015.768

AMA Style

Ennaifer R, Bacha D, Romdhane H, Cheikh M, Ben Nejma H, BelHadj N. Budd-Chiari Syndrome: An Unusual Presentation of Multisystemic Sarcoidosis. Clinics and Practice. 2015; 5(3):768. https://doi.org/10.4081/cp.2015.768

Chicago/Turabian Style

Ennaifer, Rym, Dhouha Bacha, Hayfa Romdhane, Myriam Cheikh, Houda Ben Nejma, and Najet BelHadj. 2015. "Budd-Chiari Syndrome: An Unusual Presentation of Multisystemic Sarcoidosis" Clinics and Practice 5, no. 3: 768. https://doi.org/10.4081/cp.2015.768

APA Style

Ennaifer, R., Bacha, D., Romdhane, H., Cheikh, M., Ben Nejma, H., & BelHadj, N. (2015). Budd-Chiari Syndrome: An Unusual Presentation of Multisystemic Sarcoidosis. Clinics and Practice, 5(3), 768. https://doi.org/10.4081/cp.2015.768

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