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Neurology International
Volume 3
Issue 1
10.4081/ni.2011.e3
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Neurology International is published by MDPI from Volume 12 Issue 3 (2020). Previous articles were published by another publisher in Open Access under a CC-BY licence, and they are hosted by MDPI on mdpi.com as a courtesy and upon agreement with PAGEPress.
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Case Report

Moyamoya Syndrome in an Adult with Essential Thrombocythemia

by
Marc A. Lazzaro
1,*,
Elizabeth J. Cochran
2,
Demetrius K. Lopes
3 and
Shyam Prabhakaran
4
1
Department of Neurology, Medical College of Wisconsin and Froedtert Hospital, 9200 West Wisconsin Avenue, Milwaukee, WI 53226, USA
2
Department of Pathology, Medical College of Wisconsin and Froedtert Hospital, Milwaukee, WI, USA
3
Department of Neurosurgery, Rush University Medical Center, Chicago, IL, USA
4
Department of Neurological Sciences, Section of Cerebrovascular Disease, Rush University Medical Center, Chicago, IL, USA
*
Author to whom correspondence should be addressed.
Neurol. Int. 2011, 3(1), e3; https://doi.org/10.4081/ni.2011.e3
Submission received: 23 October 2010 / Revised: 10 January 2011 / Accepted: 16 April 2011 / Published: 28 April 2011

Abstract

Moyamoya syndrome is a rare cerebrovascular disorder characterized by progressive occlusion of the supraclinoid internal carotid artery and proximal portions of the anterior and middle cerebral arteries resulting in an extensive network of collateralized blood vessels and producing a characteristic angiographic appearance. Although the pathophysiology is unclear, hematologic disorders have been associated with development of the moyamoya syndrome. A case report is presented. A 29 year-old female with a history of essential thrombocythemia developed progressive ischemic strokes. Angiography revealed characteristic moyamoya changes and pathologic examination showed intimal hyperplasia with scant collagen fibers and myxoid change. This is the first reported case of moyamoya syndrome in an adult patient with essential thrombocythemia demonstrating histological findings that suggest a shared pathophysiology with moyamoya syndrome in sickle cell anemia.
Keywords: stroke; moyamoya; essential thrombocythemia stroke; moyamoya; essential thrombocythemia

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MDPI and ACS Style

Lazzaro, M.A.; Cochran, E.J.; Lopes, D.K.; Prabhakaran, S. Moyamoya Syndrome in an Adult with Essential Thrombocythemia. Neurol. Int. 2011, 3, e3. https://doi.org/10.4081/ni.2011.e3

AMA Style

Lazzaro MA, Cochran EJ, Lopes DK, Prabhakaran S. Moyamoya Syndrome in an Adult with Essential Thrombocythemia. Neurology International. 2011; 3(1):e3. https://doi.org/10.4081/ni.2011.e3

Chicago/Turabian Style

Lazzaro, Marc A., Elizabeth J. Cochran, Demetrius K. Lopes, and Shyam Prabhakaran. 2011. "Moyamoya Syndrome in an Adult with Essential Thrombocythemia" Neurology International 3, no. 1: e3. https://doi.org/10.4081/ni.2011.e3

APA Style

Lazzaro, M. A., Cochran, E. J., Lopes, D. K., & Prabhakaran, S. (2011). Moyamoya Syndrome in an Adult with Essential Thrombocythemia. Neurology International, 3(1), e3. https://doi.org/10.4081/ni.2011.e3

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